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  • 兔抗SGCG多克隆抗體

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    • 品牌 : 通蔚生物
    • 目錄號 : TW21075
    • 應用 : 僅供科研使用
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中文名稱:  兔抗SGCG多克隆抗體  

英文名稱: Anti-SGCG rabbit polyclonal antibody

別    名: A4; MAM; DMDA; SCG3; 35DAG; DAGA4; DMDA1; LGMD2C; SCARMD2; gamma-SG

相關類別: 一抗

抗    原: SGCG

儲    存 冷凍(-20℃)

宿    主 Rabbit

反應種屬: Human, Mouse

標 記 物: Unconjugate

克隆類型: rabbit polyclonal

技術規(guī)格

Background:

This gene encodes gamma-sarcoglycan, one of several sarcolemmal transmembrane glycoproteins that interact with dystrophin. The dystrophin-glycoprotein complex (DGC) spans the sarcolemma and is comprised of dystrophin, syntrophin, alpha- and beta-dystroglycans and sarcoglycans. The DGC provides a structural link between the subsarcolemmal cytoskeleton and the extracellular matrix of muscle cells. Defects in the encoded protein can lead to early onset autosomal recessive muscular dystrophy, in particular limb-girdle muscular dystrophy, type 2C (LGMD2C).

Applications:

ELISA, WB

Name of antibody:

SGCG

Immunogen:

Synthetic peptide of human SGCG

Full name:

sarcoglycan gamma

Synonyms:

A4; MAM; DMDA; SCG3; 35DAG; DAGA4; DMDA1; LGMD2C; SCARMD2; gamma-SG

SwissProt:

Q13326

ELISA Recommended dilution:

5000-10000

WB Predicted band size:

32 kDa

WB Positive control:

Human heart tissue and Mouse heart tissue lysates

WB Recommended dilution:

200-1000